Publications: Dr Paul Telfer

Summers K, Agrippa O, Anie KA, Telfer P, Lugthart S ( 2024 ) . A Virtual Hospital Approach in Sickle Cell Disease | Remote Biometric, Quality of Life, and Hospitalisations Monitoring . Blood vol. 144 , ( Supplement 1 ) 5072 - 5072 .

Lai A, Summers K, Agrippa O, Anie KA, Telfer P, Lugthart S ( 2024 ) . Comparison of Sickle Cell Disease Patient Experiences in Developed and Developing Countries: Insights from UK and India Patient Cohorts . Blood vol. 144 , ( Supplement 1 ) 5071 - 5071 .

Frangoul H, Locatelli F, Sharma A, Bhatia M, Mapara MY, Liem RI, Wall D, Molinari L et al. ( 2024 ) . Durable Clinical Benefits with Exagamglogene Autotemcel for Severe Sickle Cell Disease . Blood vol. 144 , ( Supplement 1 ) 4954 - 4954 .

Summers KZ, Agrippa O, Ade-Odunlade D, Anie KA, Telfer P, Lugthart S ( 2024 ) . Enhanced Artificial Intelligence (AI)-Driven Prediction of Vaso-Occlusive Crises in Sickle Cell Disease: Precision through Advanced Machine-Learning Frameworks and Digital Remote Monitoring . Blood vol. 144 , ( Supplement 1 ) 522 - 522 .

Brown C, Davis M, Achebe M, Hassab H, Al-Kindi S, Telfer P, Biemond BJ, Lipato T et al. ( 2024 ) . Over 4 Years of Safety and Efficacy with Voxelotor in Patients with Sickle Cell Disease . Journal of Sickle Cell Disease vol. 1 , ( Supplement_1 )

Achebe M, Hassab H, Al-Kindi S, Brown C, Telfer P, Biemond B, Lipato T, Davis M et al. ( 2024 ) . Tolérance et efficacité de voxelotor sur une période de plus de 4ans chez les patients atteints de drépanocytose : résultats actualisés d’une étude d’extension en ouvert de l’essai de phase 3 HOPE . La Revue de Médecine Interne vol. 45 , a130 - a131 .

Frangoul H, Locatelli F, Sharma A, Bhatia M, Mapara M, Molinari L, Wall D, Liem RI et al. ( 2024 ) . Exagamglogene Autotemcel for Severe Sickle Cell Disease . New England Journal of Medicine vol. 390 , ( 18 ) 1649 - 1662 .

Telfer P, Anie KA, Kotsiopoulou S, Aiken L, Hibbs S, Burt C, Stuart-Smith S, Lugthart S ( 2024 ) . The acute pain crisis in sickle cell disease: What can be done to improve outcomes? . Blood Reviews vol. 65 ,

Frangoul H, Locatelli F, Sharma A, Bhatia M, Mapara MY, Molinari L, Wall DA, Liem R et al. ( 2024 ) . Elimination of Vaso-Occlusive Crises after Exagamglogene Autotemcel in Patients with Severe Sickle Cell Disease . Transplantation and Cellular Therapy vol. 30 , ( 2 ) s234 - s235 .

Frangoul H, Locatelli F, Sharma A, Bhatia M, Mapara M, Molinari L, Wall D, Liem RI et al. ( 2023 ) . Exagamglogene Autotemcel for Severe Sickle Cell Disease . Blood vol. 142 , ( Supplement 1 )

Achebe MO, Hassab HM, Al-Kindi S, Brown C, Telfer P, Biemond BJ, Lipato T, Davis M et al. ( 2023 ) . Over 4 Years of Safety and Efficacy with Voxelotor Treatment for Patients with Sickle Cell Disease: Updated Results from an Open-Label Extension of the Phase 3 HOPE Trial . Blood vol. 142 , ( Supplement 1 )

Summers K, Agrippa O, Lugthart S, Anie K, Telfer P ( 2023 ) . Predicting Vaso-Occlusive Crises in Sickle Cell Disease through Digital, Longitudinal Tracking of Wearable Metrics and Patient-Reported Outcomes . Blood vol. 142 , ( Supplement 1 )

Summers K, Agrippa O, Shastri O, Sharif S, Anie K, Telfer P, Lugthart S ( 2023 ) . Real-World Outcomes and Digitally Monitored Quality of Life in Voxelotor-Treated Patients with Sickle Cell Disease . Blood vol. 142 , ( Supplement 1 )

Gorur V, Kranc KR, Ganuza M, Telfer P ( 2023 ) . Haematopoietic stem cell health in sickle cell disease and its implications for stem cell therapies and secondary haematological disorders . Blood Reviews vol. 63 ,

Rankine-Mullings A, Keenan R, Chakravorty S, Inusa B, Telfer P, Velangi M, Ware RE, Moss JJ et al. ( 2023 ) . Efficacy, safety, and pharmacokinetics of a new, ready-to-use, liquid hydroxyurea in children with sickle cell anemia . Blood Advances vol. 7 , ( 16 ) 4319 - 4322 .

Ramalli M, Sangarappillai C, Kaya B, Barrosso F, Bennett S, Kafuko D, Bestwick JW, Telfer P ( 2023 ) . P1428: PREDICTORS OF VOC RATE DURING LONG‐TERM FOLLOW‐UP OF PATIENTS WITH HBSS IN A NEWBORN COHORT STUDY . HemaSphere vol. 7 , ( Suppl )

Summers K, Agrippa O, Anie K, Telfer P, Lugthart S ( 2023 ) . P1441: REAL‐WORLD OUTCOMES AND DIGITALLY MONITORED QUALITY OF LIFE IN CRIZANLIZUMAB‐TREATED PATIENTS WITH SICKLE CELL DISEASE . HemaSphere vol. 7 , ( Suppl )

Summers K, Agrippa O, Anie K, Telfer P, Lugthart S ( 2023 ) . P1448: CHARACTERISATION OF QUALITY OF LIFE‐LINKED PATIENT‐REPORTED OUTCOMES THROUGH A DIGITAL AND CONTINUOUS REMOTE MONITORING ECOSYSTEM IN SICKLE CELL DISEASE . HemaSphere vol. 7 , ( Suppl )

Badat M, Ejaz A, Hua P, Rice S, Zhang W, Hentges LD, Fisher CA, Denny N et al. ( 2023 ) . Direct correction of haemoglobin E β-thalassaemia using base editors . Nature Communications vol. 14 , ( 1 )

Telfer PT, Carvalho SJC, Ruzangi JR, Arici MA, Binns MB, Beaubrun AB, Rice CTR, Were JJW ( 2023 ) . 5554869 ASSOCIATION BETWEEN HEMOGLOBIN LEVELS AND END‐ORGAN DAMAGE IN SICKLE CELL DISEASE: A RETROSPECTIVE LINKED PRIMARY AND SECONDARY CARE DATABASE ANALYSIS IN ENGLAND . HemaSphere vol. 7 , ( Suppl ) 9 - 9 .

Agrippa OA, Summers KZ, Anie KA, Telfer P, Lugthart S ( 2023 ) . 5609968 REAL‐WORLD PATIENT‐REPORTED OUTCOMES AND WEARABLE METRIC CORRELATIONS: REMOTE DAILY MONITORING FOR EXPLORATION OF QUALITY OF LIFE IN SICKLE CELL DISEASE . HemaSphere vol. 7 , ( Suppl ) 8 - 9 .

Agrippa OA, Summers KZ, Anie KA, Telfer P, Lugthart S ( 2023 ) . 5610107 LIVE OUTCOMES AND BIOMETRIC MONITORING: POTENTIAL IMPLICATIONS FOR PATIENT QUALITY OF LIFE IN SICKLE CELL DISEASE . HemaSphere vol. 7 , ( Suppl ) 54 - 54 .

Eleftheriou P, Sharif J, Kesse‐Adu R, Filian‐Gloor M, Agrawal A, Barcelos G, Telfer P ( 2023 ) . 5613294 BASELINE PATIENT CHARACTERISTICS FROM A UK EARLY ACCESS TO MEDICINES SCHEME (EAMS) WITH VOXELOTOR, A HBS POLYMERIZATION INHIBITOR, FOR THE TREATMENT OF HEMOLYTIC ANEMIA DUE TO SICKLE CELL DISEASE . HemaSphere vol. 7 , ( Suppl ) 16 - 17 .

Telfer P, Ruzangi J, Carvalho SJ, Barcelos G, Binns M, Beaubrun A, Rice C ( 2023 ) . 5613396 DIFFERENCE IN HOSPITALIZATIONS AND ANNUAL BED DAYS FOR PATIENTS WITH SICKLE CELL DISEASE BY VARYING LEVELS OF ANEMIA: A RETROSPECTIVE ANALYSIS OF LINKED PRIMARY AND SECONDARY CARE DATABASES IN ENGLAND . HemaSphere vol. 7 , ( Suppl ) 32 - 33 .

Sangarappillai C, Ramalli M, Kaya B, Barroso F, Bennett S, Kafuko D, Bestwick J, Telfer P ( 2023 ) . Incidence rates for acute complications in HbSS East London newborn sickle cell cohort (ELNSCS) . BRITISH JOURNAL OF HAEMATOLOGY . vol. 201 , 40 - 40 .

Eleftheriou P, Sharif J, Kesse-Adu R, Drasar E, de Kreuk A, Filian-Gloor M, Agrawal A, Barcelos G et al. ( 2023 ) . Treatment of sickle cell disease with Voxelotor through the UK early access to medicines scheme . BRITISH JOURNAL OF HAEMATOLOGY . vol. 201 , 5 - 6 .

Telfer P, Carvalho SJ, Ruzangi J, Cissé OA, Binns M, Beaubrun A, Rice C, Were J ( 2022 ) . Association entre le taux d’hémoglobine et les atteintes d’organes cibles dans la drépanocytose : analyse rétrospective d’une base de données de soins primaires et secondaires en Angleterre . La Revue de Médecine Interne vol. 43 ,

Telfer P, Carvalho S, Ruzangi J, Arici M, Binns M, Beaubrun A, Montealegre-Golcher F, Rice C et al. ( 2022 ) . ASSOCIATION BETWEEN HEMOGLOBIN LEVELS AND END-ORGAN DAMAGE IN SICKLE CELL DISEASE: A RETROSPECTIVE LINKED PRIMARY AND SECONDARY CARE DATABASE ANALYSIS IN ENGLAND . Hematology Transfusion and Cell Therapy vol. 44 , s10 - s11 .

O. A, K. S, K. A, P. T, J. J, E. L ( 2022 ) . P‐037: EXPLORATION OF THE REAL‐WORLD IMPACTS OF SLEEP UPON QUALITY OF LIFE IN PATIENTS WITH SICKLE CELL DISEASE . HemaSphere vol. 6 , ( Suppl ) 35 - 35 .

Telfer P, Carvalho S, Ruzangi J, Arici M, Binns M, Beaubrun A, Rice C, Were JJ ( 2022 ) . P1488: ASSOCIATION BETWEEN HEMOGLOBIN LEVELS AND END‐ORGAN DAMAGE IN SICKLE CELL DISEASE: A RETROSPECTIVE LINKED PRIMARY AND SECONDARY CARE DATABASE ANALYSIS IN ENGLAND . HemaSphere vol. 6 , ( Suppl ) 1370 - 1371 .

Sangarappillai C, Soriano M, Bestwick J, Kafuko D, Newell K, Kaya B, Bennett S, Barroso F et al. ( 2022 ) . P1493: CHRONIC COMPLICATIONS IN THE EAST LONDON SICKLE NEWBORN COHORT STUDY (ELSNCS) . HemaSphere vol. 6 , ( Suppl ) 1375 - 1376 .

Achebe M, Hassab H, Alkindi S, Brown C, Telfer P, Biemond B, Gordeuk V, Lipato T et al. ( 2022 ) . Sécurité et efficacité à long terme du voxelotor chez des patients atteints de drépanocytose : résultats d’une étude d’extension en ouvert de l’essai de phase 3 HOPE . La Revue de Médecine Interne vol. 43 ,

Agrippa O, Summers K, Anie K, Telfer P, James J, Low E ( 2022 ) . P131: REAL‐TIME VACCINATION IMPACTS IN SICKLE CELL DISEASE: A REAL‐WORLD PATIENT CASE STUDY FOR INFLUENZA AND COVID‐19 VACCINATION . HemaSphere vol. 6 , ( Suppl ) 32 - 33 .

Lugthart S, Kotsiopoulou S, Luqmani A, Eleftheriou P, Drasar E, Brown R, Webster A, Chakravorty S et al. ( 2022 ) . S110: ACUTE AND CHRONIC PAIN MANAGEMENT IN SICKLE CELL DISEASE: OUTCOMES OF AN ENGLISH NATIONAL AUDIT . HemaSphere vol. 6 , ( Suppl ) 6 - 6 .

Achebe M, Nduba V, Hassab H, Alkindi S, Brown R, Telfer P, Biemond B, Gordeuk V et al. ( 2022 ) . S118: LONG‐TERM SAFETY AND EFFICACY OF VOXELOTOR FOR PATIENTS WITH SICKLE CELL DISEASE: RESULTS FROM AN OPEN‐LABEL EXTENSION OF THE PHASE 3 HOPE TRIAL . HemaSphere vol. 6 , ( Suppl ) 9 - 10 .

Oyesanya F, Gorur V, Awe E, Barroso F, Bennett S, Kaya B, De Michele C-A, Newell K et al. ( 2022 ) . A retrospective comparative study of the effect of automated exchange transfusion <i>versus</i> other treatment modalities on vaso-occlusive crisis admission rates in patients with sickle cell disease . BRITISH JOURNAL OF HAEMATOLOGY . vol. 197 , 138 - 139 .

Lugthart S, Kotsiopoulou S, Luqmani A, Eleftheriou P, Drasar E, Brown R, Webster A, Chakravorty S et al. ( 2022 ) . Challenges of acute and chronic pain management in sickle cell disease: Outcomes of an English national audit . BRITISH JOURNAL OF HAEMATOLOGY . vol. 197 , 11 - 12 .

Achebe M, Hassab H, Alkindi S, Brown RCC, Telfer P, Biemond BJ, Gordeuk VR, Lipato T et al. ( 2021 ) . Long-Term Safety and Efficacy of Voxelotor for Patients with Sickle Cell Disease: Results from an Open-Label Extension of the Phase 3 HOPE Trial . Blood vol. 138 , ( Supplement 1 )

Colombatti R, Sangarappillai C, Soriano M, Bestwick J, Hann W, Wieczorek K, Munaretto V, Coppadoro B et al. ( 2021 ) . Severe Acute Complications of Sickle Cell Disease in Two Expert Referral Centers (UK and Italy): Natural History Studies Highlight Ongoing Unmet Need for Effective Disease Modifying or Curative Therapies . Blood vol. 138 , ( Supplement 1 )

Shah F, Telfer P, Velangi M, Pancham S, Wynn R, Pollard S, Chalmers E, Kell J et al. ( 2021 ) . Routine management, healthcare resource use and patient and carer‐reported outcomes of patients with transfusion‐dependent β‐thalassaemia in the United Kingdom: A mixed methods observational study . eJHaem vol. 2 , ( 4 ) 738 - 749 .

Telfer P, Bestwick J, Elander J, Osias A, Khalid N, Skene I, Nzouakou R, Challands J et al. ( 2021 ) . A non-injected opioid analgesia protocol for acute pain crisis in adolescents and adults with sickle cell disease . British Journal of Pain vol. 16 , ( 2 ) 179 - 190 .

Hossain MS, Mahbub Hasan M, Petrou M, Telfer P, Mosabbir AA ( 2021 ) . The parental perspective of thalassaemia in Bangladesh: lack of knowledge, regret, and barriers . Orphanet Journal of Rare Diseases vol. 16 , ( 1 )

Chen F, Booth C, Barroso F, Bennett S, Kaya B, Win N, Telfer P ( 2021 ) . Salvage of refractory post‐transfusion hyperhaemolysis by targeting hyperinflammation and macrophage activation with tocilizumab . Transfusion Medicine vol. 32 , ( 5 ) 437 - 440 .

de la Fuente J, Gluckman E, Makani J, Telfer P, Faulkner L, Corbacioglu S, Transplantation PDWPOTESFBAM, Amrolia P et al. ( 2020 ) . The role of haematopoietic stem cell transplantation for sickle cell disease in the era of targeted disease-modifying therapies and gene editing . The Lancet Haematology vol. 7 , ( 12 ) e902 - e911 .

Vichinsky E, Gordeuk VR, Telfer P, Inati A, Tonda M, Gray S, Agodoa I, Ataga KI ( 2020 ) . Higher Hemoglobin Levels Achieved with Voxelotor Are Associated with Lower Vaso-occlusive Crisis Incidence: 72-Week Analysis from the HOPE Study . Blood vol. 136 , ( Supplement 1 ) 31 - 32 .

Smith WR, Hankins JS, Abboud MR, Cong Z, Sorof J, Gray S, Hoppe C, Telfer P ( 2020 ) . Improvement in the Clinical Global Impression of Change with Voxelotor in Patients with Sickle Cell Disease in the Phase 3 HOPE Trial . Blood vol. 136 , ( Supplement 1 ) 5 - 6 .

Jobanputra M, Paramore C, Laird SG, McGahan M, Telfer P ( 2020 ) . Co‐morbidities and mortality associated with transfusion‐dependent beta‐thalassaemia in patients in England: a 10‐year retrospective cohort analysis . British Journal of Haematology vol. 191 , ( 5 ) 897 - 905 .

Telfer P, De la Fuente J, Sohal M, Brown R, Eleftheriou P, Roy N, Piel FB, Chakravorty S et al. ( 2020 ) . Real-time national survey of COVID-19 in hemoglobinopathy and rare inherited anemia patients . Haematologica vol. 105 , ( 11 ) 2651 - 2654 .

Kountouris P, Michailidou K, Christou S, Hadjigavriel M, Sitarou M, Kolnagou A, Kleanthous M, Telfer P ( 2020 ) . Effect of HBB genotype on survival in a cohort of transfusion-dependent thalassemia patients in Cyprus . Haematologica vol. 106 , ( 9 ) 2458 - 2468 .

Maggio A, Kattamis A, Felisi M, Reggiardo G, El-Beshlawy A, Bejaoui M, Sherief L, Christou S et al. ( 2020 ) . Evaluation of the efficacy and safety of deferiprone compared with deferasirox in paediatric patients with transfusion-dependent haemoglobinopathies (DEEP-2): a multicentre, randomised, open-label, non-inferiority, phase 3 trial . The Lancet Haematology vol. 7 , ( 6 ) e469 - e478 .

Roy NBA, Telfer P, Eleftheriou P, de la Fuente J, Drasar E, Shah F, Roberts D, Atoyebi W et al. ( 2020 ) . Protecting vulnerable patients with inherited anaemias from unnecessary death during the COVID‐19 pandemic . British Journal of Haematology vol. 189 , ( 4 ) 635 - 639 .

Oakley LL, Awogbade M, Brien S, Briley A, Chorozoglou M, Drasar E, Johns J, Rhodes E et al. ( 2020 ) . Serial prophylactic exchange blood transfusion in pregnant women with sickle cell disease (TAPS-2): study protocol for a randomised controlled feasibility trial . Trials vol. 21 , ( 1 )

DeBaun MR, Jordan LC, King AA, Schatz J, Vichinsky E, Fox CK, McKinstry RC, Telfer P et al. ( 2020 ) . American Society of Hematology 2020 guidelines for sickle cell disease: prevention, diagnosis, and treatment of cerebrovascular disease in children and adults . Blood Advances vol. 4 , ( 8 ) 1554 - 1588 .

Hossain MS, Hasan MM, Raheem E, Islam MS, Al Mosabbir A, Petrou M, Telfer P, Siddiqee MH ( 2020 ) . Lack of knowledge and misperceptions about thalassaemia among college students in Bangladesh: a cross-sectional baseline study . Orphanet Journal of Rare Diseases vol. 15 , ( 1 )

Sangarappillai C, Soriano M, Telfer P, Newell K, Amoh I, Halbert J, Ndifor N, Kaya B et al. ( 2020 ) . Hydroxyurea therapy does not impact TCD velocity in the East London sickle cell newborn cohort study . BRITISH JOURNAL OF HAEMATOLOGY . vol. 189 , 146 - 147 .

Booth CS, Barroso F, Bennett S, Kafuko D, Telfer P, Kaya B ( 2020 ) . Rh antibodies in patients with sickle cell disease - an on-going challenge . BRITISH JOURNAL OF HAEMATOLOGY . vol. 189 , 166 - 166 .

Renedo A, Miles S, Chakravorty S, Leigh A, Telfer P, Warner JO, Marston C ( 2019 ) . Not being heard: barriers to high quality unplanned hospital care during young people’s transition to adult services – evidence from ‘this sickle cell life’ research . BMC Health Services Research vol. 19 , ( 1 )

Vichinsky EP, Telfer P, Inati A, Tonda M, Tong B, Agodoa I, Lehrer-Graiwer J, Ataga KI ( 2019 ) . Incidence of Vaso-Occlusive Crisis Does Not Increase with Achieving Higher Hemoglobin Levels on Voxelotor Treatment or after Discontinuation: Analyses of the HOPE Study . Blood vol. 134 , ( Supplement_1 )

Shah F, Telfer P, Velangi M, Pancham S, Wynn R, Pollard S, Chalmers E, Kell J et al. ( 2019 ) . Routine Management, Healthcare Resource Use and Patient/Caregiver-Reported Outcomes of Patients with Transfusion-Dependent β-Thalassaemia in the United Kingdom: A Mixed Methods Observational Study . Blood vol. 134 , ( Supplement_1 )

Ryan K, Pancham S, Telfer P, Shah F, Kell J, Pollard S, Wynn R, Velangi M et al. ( 2019 ) . PRO146 HEALTH-RELATED QUALITY OF LIFE AND PRODUCTIVITY/ACTIVITY IMPAIRMENT IN PATIENTS WITH TRANSFUSION DEPENDENT B-THALASSAEMIA IN THE UK NHS: DATA FROM A UK MULTICENTRE OBSERVATIONAL STUDY . Value in Health vol. 22 , s868 - s869 .

Telfer P, Barroso F, Newell K, Challands J, Kaya B ( 2019 ) . Evaluation of a Non-Parenteral Opioid Analgesia Protocol for Acute Sickle Cell Pain Episodes in Children . Journal of Clinical Medicine vol. 8 , ( 10 )

Downes M, de Haan M, Telfer PT, Kirkham FJ ( 2019 ) . The Role of Family Functioning in the Development of Executive Functions in Preschool Children with Sickle Cell Anemia . Developmental Neuropsychology vol. 44 , ( 6 ) 452 - 467 .

Telfer PT ( 2019 ) . Management of sickle cell disease: management of acute episodes in the community and in hospital . Paediatrics and Child Health vol. 29 , ( Br J Haematol 120 2003 ) 345 - 351 .

Kaya B, Telfer PT ( 2019 ) . Management of sickle cell disease: outpatient and community aspects . Paediatrics and Child Health vol. 29 , ( N Engl J Med 339 1998 Jul 2 ) 352 - 358 .

Telfer P, Kountouris P, Christou S, Hadjigavriel M, Sitarou M, Kolnagou A, Kleanthous M ( 2019 ) . PF785 CHANGING CAUSES OF MORTALITY IN TDT DURING THE ERA OF ORAL CHELATION THERAPY FROM 2000 TO 2018 . HemaSphere vol. 3 , ( S1 ) 346 - 347 .

Kattamis A, Felisi M, Reggiardo G, El‐Beshlawy A, Bejaoui M, Sherief L, Christou S, Cosmi C et al. ( 2019 ) . S144 A MULTICENTRE, RANDOMIZED, NON‐INFERIORITY TRIAL COMPARING THE EFFICACY OF DEFERIPRONE VERSUS DEFERASIROX IN PEDIATRIC PATIENTS AFFECTED BY TRANSFUSION‐DEPENDENT HEMOGLOBINOPATHIES (DEEP‐2 TRIAL) . HemaSphere vol. 3 , ( S1 ) 23 - 24 .

Vichinsky E, Hoppe CC, Ataga KI, Ware RE, Nduba V, Beshlawy AE, Hassab H, Achebe MM et al. ( 2019 ) . S147 RESULTS FROM THE RANDOMIZED PLACEBO‐CONTROLLED PHASE 3 HOPE TRIAL OF VOXELOTOR IN ADULTS AND ADOLESCENTS WITH SICKLE CELL DISEASE . HemaSphere vol. 3 , ( S1 ) 25 - 26 .

Elander J, Bij D, Kapadi R, Schofield MB, Osias A, Khalid N, Kaya B, Telfer P ( 2019 ) . Development and validation of the Satisfaction with Treatment for Pain Questionnaire (STPQ) among patients with sickle cell disease . British Journal of Haematology . vol. 187 , 105 - 116 .

Vichinsky E, Hoppe CC, Ataga KI, Ware RE, Nduba V, El-Beshlawy A, Hassab H, Achebe MM et al. ( 2019 ) . A Phase 3 Randomized Trial of Voxelotor in Sickle Cell Disease . New England Journal of Medicine vol. 381 , ( 6 ) 509 - 519 .

Cooper O, McBain H, Tangayi S, Telfer P, Tsitsikas D, Yardumian A, Mulligan K ( 2019 ) . Psychometric analysis of the adult sickle cell quality of life measurement information system (ACSQ-Me) in a UK population . Health and Quality of Life Outcomes vol. 17 , ( 1 )

Mecci J, Maxan M-E, Kemos P, Telfer P, Barroso F, Foster G, Banu K ( 2019 ) . FRI-437-Diagnosis of sickle cell liver disease may be aided by non-invasive tests . Journal of Hepatology . vol. 70 , e586 - e587 .

Brown RA, Moon JC, Telfer PT, Khanji MY ( 2019 ) . Extreme cardiac iron loading in transfusion-dependent thalassaemia major: cardiac T2* and T1 mapping guiding treatment . European Heart Journal vol. 40 , ( 43 ) 3578 - 3578 .

Howard J, Hemmaway CJ, Telfer P, Layton DM, Porter J, Awogbade M, Mant T, Gretler DD et al. ( 2019 ) . A phase 1/2 ascending dose study and open-label extension study of voxelotor in patients with sickle cell disease . Blood vol. 133 , ( 17 ) 1865 - 1875 .

Telfer P, Kaya B, Barroso F, Nzouakou R, Osias A, Bloom B, Skene I, Boulton O et al. ( 2019 ) . A Phase 1 study to determine maximum tolerated dose of sublingual fentanyl in combination with oral oxycodone for hospital management of an acute painful crisis in adolescents and adults with sickle cell disease . BRITISH JOURNAL OF HAEMATOLOGY . vol. 185 , 113 - 114 .

Ryan K, Pancham S, Telfer P, Shah F, Kell J, Pollard S, Wynn R, Velangi M et al. ( 2019 ) . An observational study to evaluate the routine management, healthcare resource use and outcomes for patients with transfusion-dependent β-thalassaemia treated in the United Kingdom: an interim analysis . BRITISH JOURNAL OF HAEMATOLOGY . vol. 185 , 114 - 115 .

Mckinnon K, Telfer P, Kaya B ( 2019 ) . Causes, management and outcomes of extreme paediatric thrombocytosis . BRITISH JOURNAL OF HAEMATOLOGY . vol. 185 , 108 - 108 .

Ryan K, Pancham S, Telfer P, Shah F, Kell J, Pollard S, Wynn R, Velangi M et al. ( 2019 ) . HEALTH-RELATED QUALITY OF LIFE AND PRODUCTIVITY/ACTIVITY IMPAIRMENT IN PATIENTS WITH TRANSFUSION DEPENDENT B-THALASSAEMIA IN THE UK NHS: DATA FROM A UK MULTICENTRE OBSERVATIONAL STUDY . VALUE IN HEALTH . vol. 22 , S868 - S869 .

Sangarappillai C, Kaya B, Barroso F, Telfer P ( 2019 ) . Patients lost to follow-up in the East London Newborn Sickle Cell Cohort Study . BRITISH JOURNAL OF HAEMATOLOGY . vol. 185 , 123 - 124 .

Okochi J, Tsiagbe M, Joseph W, James J, Osmond-Joseph K, Telfer P, Barroso F, Kaya B ( 2019 ) . Peer to peer mentoring for patients with Sickle Cell Disease - interim analysis of results from a pilot programme in East London . BRITISH JOURNAL OF HAEMATOLOGY . vol. 185 , 116 - 116 .

Downes M, de Haan M, O’Leary T, Telfer PT, Kirkham FJ ( 2018 ) . Temperament in preschool children with sickle cell anaemia . Archives of Disease in Childhood vol. 105 , ( 9 ) 900 - 902 .

Telfer P, Kaya B, Tsitsikas DA, Barroso F, Sangarappillai C ( 2018 ) . Hydroxyurea Therapy Does Not Impact Current Survival Estimates in the East London Sickle Cell Newborn Cohort Study . Blood vol. 132 , ( Supplement 1 )

Vichinsky E, Hoppe C, Howard J, Ataga KI, Nduba V, El-Beshlawy A, Diuguid DL, Al-Kindi S et al. ( 2018 ) . Results from Part A of the Hemoglobin Oxygen Affinity Modulation to Inhibit HbS Polymerization (HOPE) Trial (GBT440-031), a Placebo-Controlled Randomized Study Evaluating Voxelotor (GBT440) in Adults and Adolescents with Sickle Cell Disease . Blood . vol. 132 ,

Casella JF, Adams RJ, Brambilla DJ, Strouse JJ, Maier P, Dlugash R, Avadhani R, Vermillion K et al. ( 2018 ) . Developing a risk-based composite neurologic outcome for a trial of hydroxyurea in young children with sickle cell disease . Clinical Trials vol. 16 , ( 1 ) 20 - 31 .

Lobitz S, Telfer P, Cela E, Allaf B, Angastiniotis M, Johansson CB, Badens C, Bento C et al. ( 2018 ) . Newborn screening for sickle cell disease in Europe: recommendations from a Pan‐European Consensus Conference . British Journal of Haematology vol. 183 , ( 4 ) 648 - 660 .

Telfer PT, Devereux H, Savage K, Scott F, Dhillon AP, Dusheiko G, Lee CA ( 2018 ) . Chronic Hepatitis C Virus Infection in Haemophilic Patients: Clinical Significance of Viral Genotype . Thrombosis and Haemostasis vol. 74 , ( 05 ) 1259 - 1264 .

Downes M, Kirkham FJ, Berg C, Telfer P, de Haan M ( 2018 ) . Executive performance on the preschool executive task assessment in children with sickle cell anemia and matched controls . Child Neuropsychology vol. 25 , ( 2 ) 278 - 285 .

Downes M, Kirkham FJ, Telfer PT, de Haan M ( 2018 ) . Assessment of Executive Functions in Preschool Children With Sickle Cell Anemia . Journal of the International Neuropsychological Society vol. 24 , ( 9 ) 949 - 954 .

Telfer P, Agodoa I, Fox KM, Burke L, Mant T, Jurek M, Tonda M, Lehrer-Graiwer J ( 2018 ) . Impact of voxelotor (GBT440) on unconjugated bilirubin and jaundice in sickle cell disease . Hematology Reports vol. 10 , ( 2 )

Yeo JH, Islam A, Cavenagh J, Smith M, Telfer P, Kaya B ( 2018 ) . A Case Report of Dehydrated Hereditary Stomatocytosis and Spherocytosis . BRITISH JOURNAL OF HAEMATOLOGY . vol. 181 , 125 - 125 .

Nzouakou R, Kaya B, Koomson E, Barroso F, Telfer P ( 2018 ) . Cross-over study comparing manual exchange transfusion versus automated erythrocytapheresis. Experience of a single centre . BRITISH JOURNAL OF HAEMATOLOGY . vol. 181 , 122 - 122 .

Smith C, Kawadler J, Kirkham F, Hogan A, Telfer P, Stotesbury H ( 2018 ) . Residential proximity to major roads and cognitive function in asymptomatic children with Sickle Cell Anaemia: a longitudinal study . BRITISH JOURNAL OF HAEMATOLOGY . vol. 181 , 117 - 117 .

Telfer P, Kaya B ( 2017 ) . Optimizing the care model for an uncomplicated acute pain episode in sickle cell disease . Hematology vol. 2017 , ( 1 ) 525 - 533 .

de Montalembert M, Brousse V, Chakravorty S, Pagliuca A, Porter J, Telfer P, Vora A, Rees DC ( 2017 ) . Are the risks of treatment to cure a child with severe sickle cell disease too high? . The BMJ vol. 359 ,

Downes M, Kirkham FJ, Telfer PT, de Haan M ( 2017 ) . Altered Neurophysiological Processing of Auditory Attention in Preschool Children With Sickle Cell Disease . Journal of Pediatric Psychology vol. 43 , ( 8 ) 856 - 869 .

Lehrer-Graiwer J, Howard J, Hemmaway CJ, Awogbade M, Telfer P, Layton M, Porter JB, Mant T et al. ( 2016 ) . Long-Term Dosing in Sickle Cell Disease Subjects with GBT440, a Novel HbS Polymerization Inhibitor . Blood . vol. 128 ,

Piel FB, Tewari S, Brousse V, Analitis A, Font A, Menzel S, Chakravorty S, Thein SL et al. ( 2016 ) . Associations between environmental factors and hospital admissions for sickle cell disease . Haematologica vol. 102 , ( 4 ) 666 - 675 .

Downes M, de Haan M, Kirkham FJ, Telfer PT ( 2016 ) . Parent reported sleep problems in preschool children with sickle cell anemia and controls in East London . Pediatric Blood & Cancer vol. 64 , ( 6 )

Telfer P, Dwan K, Simmons A, Evanson J, Gadong N, Newell K, Tangayi S, Leigh A et al. ( 2016 ) . Transcranial Doppler Screening in a Regional Care Network for Sickle Cell Disease in the United Kingdom . Journal of Pediatric Hematology/Oncology vol. 38 , ( 7 ) 517 - 524 .

Fisher AE, Oduro AKY, Adzaku F, Telfer P ( 2016 ) . Presentations of sickle cell disease patients to hospital in Ghana: key findings from a preliminary study at Volta Regional Hospital . British Journal of Haematology vol. 178 , ( 3 ) 489 - 491 .

Tewari S, Piel F, Brousse V, Analitis A, Ghersi V, Menzel S, Chakravorty S, Inusa B et al. ( 2016 ) . ASSOCIATION BETWEEN ENVIRONMENTAL FACTORS AND HOSPITAL ADMISSIONS FOR SICKLE CELL DISEASE: A RETROSPECTIVE TIME SERIES ANALYSIS . HAEMATOLOGICA . vol. 101 , 127 - 128 .

Nzouakou R, Newell K, Barroso F, Telfer P, Kaya B ( 2016 ) . Annual review of transfusion targets in regularly transfused paediatric and adult sickle cell patients. Experiences from Bart's Health NHS Trust . BRITISH JOURNAL OF HAEMATOLOGY . vol. 173 , 153 - 154 .

Lehrer-Graiwer J, Hemmaway C, Howard J, Telfer P, Layton M, Awogbade M, Porter J, Roberts-Harewood M et al. ( 2016 ) . GBT440, A NOVEL HBS POLYMERIZATION INHIBITOR, INCREASES HB OXYGEN AFFINITY AND RESULTS IN A RAPID IMPROVEMENT IN HEMOLYSIS AND ANEMIA . HAEMATOLOGICA . vol. 101 , 125 - 125 .

Kaya B, Telfer P ( 2016 ) . Review of an internal quality assurance programme for transcranial doppler (TCD) screening in children with sickle cell disease. Experiences from Bart's Health NHS Trust . BRITISH JOURNAL OF HAEMATOLOGY . vol. 173 , 143 - 143 .

Lehrer-Graiwer J, Howard J, Hemmaway CJ, Awogbade M, Telfer P, Layton M, Mant T, Dufu K et al. ( 2015 ) . GBT440, a Potent Anti-Sickling Hemoglobin Modifier Reduces Hemolysis, Improves Anemia and Nearly Eliminates Sickle Cells in Peripheral Blood of Patients with Sickle Cell Disease . Blood . vol. 126 ,

de la Fuente J, O'Boyle F, Harrington Y, Bradshaw A, Hing S, Chakravorty S, Karnik L, New H et al. ( 2015 ) . Haploidentical BMT with a Post-Infusion of Stem Cells Cyclophosphamide Approach Is Feasible and Leads to a High Rate of Donor Engraftment in Haemoglobinopathies Allowing Universal Application of Transplantation . Blood . vol. 126 ,

Lagunju I, Sodeinde O, Telfer P, Brown B ( 2015 ) . Transcranial doppler ultrasonography in primary stroke prevention in children with sickle cell disease: our initial experience . Archives of Disease in Childhood vol. 95 , ( Suppl 1 ) a63 - a64 .

Telfer PT ( 2015 ) . Management of sickle cell disease: management of acute episodes in the community and in hospital . Paediatrics and Child Health vol. 25 , ( 8 ) 368 - 374 .

Telfer PT ( 2015 ) . Management of sickle cell disease: out-patient and community aspects . Paediatrics and Child Health vol. 25 , ( 8 ) 375 - 380 .

Parhar K, Parizkova B, Jones N, Valchanov K, Fowles J-A, Besser M, Telfer P, Kaya B et al. ( 2015 ) . Extracorporeal membrane oxygenation for the treatment of adult sickle cell acute chest syndrome . Perfusion vol. 31 , ( 3 ) 262 - 265 .

Mian HS, Ward R, Telfer P, Kaya B, Kuo KHM ( 2015 ) . Optimal Manual Exchange Transfusion Protocol for Sickle Cell Disease: A Retrospective Comparison of Two Comprehensive Care Centers in the United Kingdom and Canada . Hemoglobin vol. 39 , ( 5 ) 310 - 315 .

Kawadler JM, Kirkham FJ, Clayden JD, Hollocks MJ, Seymour EL, Edey R, Telfer P, Robins A et al. ( 2015 ) . White Matter Damage Relates to Oxygen Saturation in Children With Sickle Cell Anemia Without Silent Cerebral Infarcts . Stroke vol. 46 , ( 7 ) 1793 - 1799 .

Badat M, Kaya B, Telfer P ( 2015 ) . Combination‐therapy with concurrent deferoxamine and deferiprone is effective in treating resistant cardiac iron‐loading in aceruloplasminaemia . British Journal of Haematology vol. 171 , ( 3 ) 430 - 432 .

Tsouana E, Kaya B, Gadong N, Hemmaway C, Newell H, Simmons A, Whitmarsh S, Telfer P ( 2015 ) . Deferasirox for iron chelation in multitransfused children with sickle cell disease; long-term experience in the East London clinical haemoglobinopathy network . Eur J Haematol vol. 94 , ( 4 ) 336 - 342 .

De Montalembert M, Abboud MR, Fiquet A, Inati A, Lebensburger JD, Kaddah N, Mokhtar G, Piga A et al. ( 2015 ) . 13‐valent pneumococcal conjugate vaccine (PCV13) is immunogenic and safe in children 6‐17 years of age with sickle cell disease previously vaccinated with 23‐valent pneumococcal polysaccharide vaccine (PPSV23): Results of a phase 3 study . Pediatric Blood & Cancer vol. 62 , ( 8 ) 1427 - 1436 .

Kuo KHM, Ward R, Kaya B, Howard J, Telfer P ( 2015 ) . A comparison of chronic manual and automated red blood cell exchange transfusion in sickle cell disease patients . British Journal of Haematology vol. 170 , ( 3 ) 425 - 428 .

Badat M, Bailey F, Syed T, Badle S, Simmons A, Kaya B, Telfer P ( 2015 ) . Effects of the 2013 MHRA update on codeine use: a retrospective study of admissions to hospital with an acute vaso-occlusive pain crisis in children with sickle cell disease . BRITISH JOURNAL OF HAEMATOLOGY . vol. 169 , 99 - 99 .

de la Fuente J, Harrington Y, Bradshaw A, Inusa B, Telfer P ( 2015 ) . Parental Haploidentical HSCT with a Post-Infusion of Stem Cells Cyclophosphamide Approach is Feasible and Leads to a High Rate of Donor Engraftment in Haemoglobinopathies Allowing Universal Application of Transplantation . BONE MARROW TRANSPLANTATION . vol. 50 , S45 - S45 .

Howard J, Telfer P ( 2015 ) . Sickle Cell Disease in Clinical Practice . Springer Nature

Telfer P, Simmons A, Gadong N, Newell K, Tangayi S, Leigh A, Vaidyanathan S, Hemmaway C et al. ( 2015 ) . Transcranial Doppler screening and residual stroke rate in UK children with sickle cell disease: data from the East London and Essex clinical haemoglobinopathy network . BRITISH JOURNAL OF HAEMATOLOGY . vol. 169 , 23 - 23 .

Fisher AE, Oduro AKY, Adzaku FK, Telfer P ( 2015 ) . Use of analgesia in sickle cell crisis at Volta Regional Hospital, Ho, Ghana . BRITISH JOURNAL OF HAEMATOLOGY . vol. 169 , 101 - 101 .

Tewari S, Piel F, Brousse V, Inusa BP, Telfer P, Menzel S, De Montalembert M, Gardner K et al. ( 2014 ) . A Multicentre Study of Environmental Factors on the Severity of Sickle Cell Disease . Blood . vol. 124 ,

Downes M, de Haan M, Kirkham FJ, Kaya B, Telfer P ( 2014 ) . Disease-Related Factors and Family Functioning As Predictors of Executive Functioning in Preschool Children with Sickle Cell Anaemia: A Preliminary Analysis . Blood vol. 124 , ( 21 )

Calvaruso G, Vitrano A, Di Maggio R, Ballas S, Steinberg MH, Rigano P, Sacco M, Telfer P et al. ( 2014 ) . Deferiprone versus deferoxamine in sickle cell disease: results from a 5-year long-term Italian multi-center randomized clinical trial . Blood Cells Mol Dis vol. 53 , ( 4 ) 265 - 271 .

DeBaun MR, Gordon M, McKinstry RC, Noetzel MJ, White DA, Sarnaik SA, Meier ER, Howard TH et al. ( 2014 ) . Controlled trial of transfusions for silent cerebral infarcts in sickle cell anemia . N Engl J Med vol. 371 , ( 8 ) 699 - 710 .

Telfer P, Bahal N, Lo A, Challands J ( 2014 ) . Management of the acute painful crisis in sickle cell disease- a re-evaluation of the use of opioids in adult patients . Br J Haematol vol. 166 , ( 2 ) 157 - 164 .

Tsouana E, Kaya B, Gadong N, Hemmaway C, Newell H, Simmons A, Whitmarsh S, Telfer P ( 2013 ) . Inadequate Long-Term Control Of Transfusion Iron Overload In Children With Sickle Cell Disease Chelated With Deferasirox . Blood vol. 122 , ( 21 )

Hogan AM, Telfer PT, Kirkham FJ, de Haan M ( 2013 ) . Precursors of Executive Function in Infants With Sickle Cell Anemia . JOURNAL OF CHILD NEUROLOGY vol. 28 , ( 10 ) 1197 - 1202 .

Maggio A, Vitrano A, Calvaruso G, Barone R, Rigano P, Mancuso L, Cuccia L, Capra M et al. ( 2013 ) . Serial echocardiographic left ventricular ejection fraction measurements: A tool for detecting thalassemia major patients at risk of cardiac death . BLOOD CELLS MOLECULES AND DISEASES vol. 50 , ( 4 ) 241 - 246 .

Kuo KHM, Ward R, Howard J, Telfer P ( 2012 ) . A Comparison of Chronic Manual and Automated Red Blood Cell Exchange Transfusion in Sickle Cell Disease Patients From Two Comprehensive Care Centres in the United Kingdom . Blood vol. 120 , ( 21 )

Dundas I, Telfer P, Rae J, Toweh G, Onyiah N, Kaya B, Newell K, Pao C et al. ( 2012 ) . A Cohort Study Of Sleep Disordered Breathing In Pre-School Children With Sickle Cell Disease . Conference: D107. PEDIATRIC SLEEP DISORDERSa6659 - a6659 .

Telfer P, Dundas I, Rae J, Toweh G, Kaya B, Newell K, Pao C, Grigg J et al. ( 2012 ) . A cohort study of sleep disordered breathing in preschool children with sickle cell disease . BRITISH JOURNAL OF HAEMATOLOGY . vol. 157 , 70 - 71 .

Mohamed M, Pratt R, Telfer P, Kaya B ( 2012 ) . Acute pain management protocols in adult sickle cell patients - audit of observation frequency following administration of opiate analgesia . BRITISH JOURNAL OF HAEMATOLOGY . vol. 157 , 74 - 75 .

Jayaratne D, Wirth L, Barber C, Kaya B, Telfer P, Allard S ( 2012 ) . Alloantibody formation in regularly transfused young patients (aged ≤ 21 years) with sickle cell disease - a single centre review . BRITISH JOURNAL OF HAEMATOLOGY . vol. 157 , 82 - 82 .

DeBaun MR, Sarnaik SA, Rodeghier MJ, Minniti CP, Howard TH, Iyer RV, Inusa B, Telfer PT et al. ( 2012 ) . Associated risk factors for silent cerebral infarcts in sickle cell anemia: low baseline hemoglobin, sex, and relative high systolic blood pressure . BLOOD vol. 119 , ( 16 ) 3684 - 3690 .

Lagunju I, Sodeinde O, Telfer P ( 2012 ) . Prevalence of transcranial Doppler abnormalities in Nigerian children with sickle cell disease . AMERICAN JOURNAL OF HEMATOLOGY vol. 87 , ( 5 ) 544 - 547 .

Mohamed M, Pratt R, Telfer P, Kaya B ( 2012 ) . Use of individualised acute pain management protocols in adult sickle cell patients - a single centre experience . BRITISH JOURNAL OF HAEMATOLOGY . vol. 157 , 75 - 75 .

Telfer PT, Evanson J, Butler P, Hemmaway C, Abdulla C, Gadong N, Whitmarsh S, Kaya B et al. ( 2011 ) . Cervical carotid artery disease in sickle cell anemia: clinical and radiological features . Blood vol. 118 , ( 23 ) 6192 - 6199 .

Telfer PT ( 2011 ) . Management of sickle cell disease: acute episodes in the community and in hospital . Paediatrics and Child Health vol. 21 , ( 8 ) 363 - 368 .

Telfer PT ( 2011 ) . Management of sickle cell disease: out-patient and community aspects . Paediatrics and Child Health vol. 21 , ( 8 ) 357 - 362 .

Kaur M, Sen G, Kaya B, Telfer P ( 2011 ) . An audit of a transfusion algorithm for use in paediatric thalassaemia patients . BRITISH JOURNAL OF HAEMATOLOGY . vol. 153 , 66 - 67 .

Obaro SK, Inusa B, Telfer P ( 2011 ) . Hydroxycarbamide use in young children with sickle-cell anaemia . LANCET vol. 378 , ( 9805 ) 1777 - 1777 .

Telfer PT, Evanson J, Hemmaway C, Abdullah C, Gadong N, Whitmarsh S, van Meijgaarden B, Kaya B et al. ( 2011 ) . Low risk of stroke in children with sickle cell disease (SCD) screened with transcranial Doppler (TCD) ultrasound . BRITISH JOURNAL OF HAEMATOLOGY . vol. 153 , 26 - 27 .

Leigh AY, Nolan A, Cryer J, Lethaby D, Doukrou M, Fulcher S, Kaya B, Simmons A et al. ( 2011 ) . Percutaneous endoscopic gastrostomy feeds in children with sickle cell disease and growth failure; a novel approach with high patient and carer satisfaction . BRITISH JOURNAL OF HAEMATOLOGY . vol. 153 , 65 - 65 .

Di Marco V, Capra M, Angelucci E, Borgna-Pignatti C, Telfer P, Harmatz P, Kattamis A, Prossamariti L et al. ( 2010 ) . Management of chronic viral hepatitis in patients with thalassemia: recommendations from an international panel . BLOOD vol. 116 , ( 16 ) 2875 - 2883 .

Telfer P, Kaya B ( 2010 ) . Management of HCV Infection in Patients with Thalassemia and Sickle Cell Disease . Clinical Dilemmas in Viral Liver Disease , Wiley

Telfer PT, Warburton F, Christou S, Hadjigavriel M, Sitarou M, Kolnagou A, Angastiniotis M ( 2009 ) . Improved survival in thalassemia major patients on switching from desferrioxamine to combined chelation therapy with desferrioxamine and deferiprone . Haematologica vol. 94 , ( 12 ) 1777 - 1778 .

Telfer P, Criddle J, Sandell J, Davies F, Morrison I, Challands J ( 2009 ) . Intranasal diamorphine for acute sickle cell pain . Arch Dis Child vol. 94 , ( 12 ) 979 - 980 .

Sarnaik SA, Casella JF, Barton BA, Afif M, Airewele G, Berman BW, Bernaudin F, Coates T et al. ( 2009 ) . Elevated Systolic Blood Pressure and Low Fetal Hemoglobin Are Risk Factors for Silent Cerebral Infarcts in Children with Sickle Cell Anemia . BLOOD . vol. 114 , 111 - 111 .

Kaya B, Heath P, Vaidya M, Telfer P ( 2009 ) . A role for non invasive ventilation for acute chest syndrome in children: our experience . BRITISH JOURNAL OF HAEMATOLOGY . vol. 145 , 73 - 73 .

McLeod C, Fleeman N, Kirkham J, Bagust A, Boland A, Chu P, Dickson R, Dundar Y et al. ( 2009 ) . Deferasirox for the treatment of iron overload associated with regular blood transfusions (transfusional hemosiderosis) in patients suffering with chronic anaemia: a systematic review and economic evaluation . Health Technology Assessment vol. 13 , ( 1 ) 1 - 144 .

Telfer P ( 2009 ) . Update on survival in thalassemia major . Hemoglobin vol. 33 Suppl 1 , S76 - S80 .

Tsitsikas DA, Barroso FA, Telfer P, Kaya B, Evanson J, Provan A ( 2008 ) . A patient with beta thalassaemia major and back pain . BMJ vol. 337 ,

Telfer P, Sabin C, Devereux H, Scott F, Dusheiko G, Lee C ( 2008 ) . The progression of HCV‐associated liver disease in a cohort of haemophilic patients . British Journal of Haematology vol. 87 , ( 3 ) 555 - 561 .

King MJ, Telfer P, MacKinnon H, Langabeer L, McMahon C, Darbyshire P, Dhermy D ( 2008 ) . Using the eosin-5-maleimide binding test in the differential diagnosis of hereditary spherocytosis and hereditary pyropoikilocytosis . CYTOM PART B-CLIN CY vol. 74B , ( 4 ) 244 - 250 .

Kirkham J, Baird J, Telfer P, Khatura J, Sahota TP, Wilkey O, Robins A, Morgan MA et al. ( 2008 ) . HEIGHT AND WEIGHT IN A UK POPULATION OF CHILDREN WITH SICKLE CELL DISEASE . HAEMATOLOGICA-THE HEMATOLOGY JOURNAL . vol. 93 , 448 - 448 .

Kirkham J, Telfer P, Bucks RS, Hewes DKM, Kaya B, Prengler M, Dundas I, Lane R et al. ( 2008 ) . OVERNIGHT OXYHAEMOGLOBIN DESATURATION PREDICTS ABNORMAL TRANSCRANIAL DOPPLER IN SICKLE CELL ANAEMIA . HAEMATOLOGICA-THE HEMATOLOGY JOURNAL . vol. 93 , 252 - 252 .

Kirkham J, Dingle-Gavlak J, Krings J, Hewes DKM, Dundas I, Lane R, Carr S, Evans JPM et al. ( 2008 ) . OXYHAEMOGLOBIN SATURATION, ASTHMA AND CHEST CRISIS IN PAEDIATRIC SICKLE CELL . HAEMATOLOGICA-THE HEMATOLOGY JOURNAL . vol. 93 , 404 - 404 .

Hogan AM, Telfer P, Prengler M, Saunders D, Wade AM, Vargha-Khadem F, Kirkham FJ ( 2008 ) . Intellectual function in children with sickle cell anemia: longitudinal data from the East London cohort . BRITISH JOURNAL OF HAEMATOLOGY . vol. 141 , 111 - 111 .

Marshall MJ, Laverty A, Dingle-Gavlak J, Kirkham FJ, Evans J, Telfer P, Wilkey O, Yardumian A et al. ( 2008 ) . Sleep-related breathing disorders in sickle cell disease . BRITISH JOURNAL OF HAEMATOLOGY . vol. 141 , 112 - 112 .

Telfer PT, Brown D, Devereux H, Lee CA, Du Sheiko GM ( 2008 ) . HCV RNA levels and HIV infection: evidence for a viral interaction in haemophilic patients . British Journal of Haematology vol. 88 , ( 2 ) 397 - 399 .

Lee C, Chrispeels J, Telfer P, Dusheiko G ( 2008 ) . HEPATITIS C ANTIBODY PROFILE IN ADULTS WITH HAEMOPHILIA AND THEIR SEXUAL PARTNERS . British Journal of Haematology vol. 81 , ( 1 ) 133 - 136 .

Alexander E, Telfer P, Rashid H, Ali KA, Booy R ( 2008 ) . Nasopharyngeal carriage rate of Streptococcus pneumoniae in children with sickle cell disease before and after the introduction of heptavalent pneumococcal conjugate vaccine . J Infect Public Health vol. 1 , ( 1 ) 40 - 44 .

Devereux H, Telfer P, Brown D, Morris A, Dusheiko G, Emery V, Lee C ( 2007 ) . Longitudinal genotype analysis and quantification of hepatitis C virus in haemophilia patients receiving interferon‐α therapy . Journal of Viral Hepatitis vol. 3 , ( 1 ) 43 - 48 .

Telfer P, Devereux H, Colvin B, Hayden S, Dusheiko G, Lee C ( 2007 ) . Alpha interferon for hepatitis C virus infection in haemophilic patients . Haemophilia vol. 1 , ( 1 ) 54 - 58 .

Telfer P, Coen P, Chakravorty S, Wilkey O, Evans J, Newell H, Smalling B, Amos R et al. ( 2007 ) . Clinical outcomes in children with sickle cell disease living in England: a neonatal cohort in East London . Haematologica vol. 92 , ( 7 ) 905 - 912 .

Hogan AM, Hill CM, Bucks R, Telfer P, Kirkham FJ ( 2007 ) . Increased cerebral blood flow velocity in children with sickle cell disease: Adenotonsillectomy or transfusion regimens? In reply . PEDIATRICS vol. 120 , ( 1 ) 236 - 237 .

MILLER R, TELFER P ( 2007 ) . HCV counselling in haemophilia care . Haemophilia vol. 2 , ( 1 ) 1 - 4 .

TELFER P ( 2007 ) . Sexual transmission of hepatitis C virus . Haemophilia vol. 1 , ( S4 ) 15 - 18 .

TELFER P ( 2007 ) . Treatment of chronic hepatitis C infection in haemophilic patients: the Royal Free and Royal London Hospital experience . Haemophilia vol. 1 , ( S4 ) 39 - 40 .

Anderson AK, Simmons A, Newell H, Fofana N, Paterson M, Telfer P ( 2007 ) . Avascular necrosis of the femoral head in HbSS children taking hydroxyurea . BRITISH JOURNAL OF HAEMATOLOGY . vol. 137 , 73 - 73 .

Lahoz C, Ali K, Challands J, Morrison I, Newell K, John Y, Telfer P ( 2007 ) . Evaluation of analgesia regime with intranasal diamorphine and oral morphine for acute painful sickle crises in children . BRITISH JOURNAL OF HAEMATOLOGY . vol. 137 , 82 - 83 .

Bhattacharya A, Newell H, Evanson J, Kirkham F, Telfer P ( 2007 ) . Extracranial carotid artery occlusion in children with sickle cell disease . BRITISH JOURNAL OF HAEMATOLOGY . vol. 137 , 73 - 73 .

Telfer P, Franklin A, Carr S, McKenzie S, Newell H, Kirkham F ( 2007 ) . Nocturnal hypoxaemia is associated with conditional and high risk transcranial doppler velocities in children with sickle cell disease . BRITISH JOURNAL OF HAEMATOLOGY . vol. 137 , 88 - 88 .

Hogan AM, Telfer P, Kirkham FJ ( 2007 ) . The impact of infection in early childhood on intellectual function in adolescence: evidence from children with sickle cell disease . BRITISH JOURNAL OF HAEMATOLOGY . vol. 137 , 29 - 29 .

Telfer P, Coen PG, Christou S, Hadjigavriel M, Kolnakou A, Pangalou E, Pavlides N, Psiloines M et al. ( 2006 ) . Survival of medically treated thalassemia patients in Cyprus. Trends and risk factors over the period 1980-2004 . Haematologica vol. 91 , ( 9 ) 1187 - 1192 .

Yakout TI, Beski S, Telfer P ( 2006 ) . Anaemia in pregnancy at the Royal London Hospital . BRITISH JOURNAL OF HAEMATOLOGY . vol. 133 , 35 - 36 .

Baldeweg T, Hogan AM, Saunders DE, Telfer P, Gadian DG, Vargha-Khadem F, Kirkham FJ ( 2006 ) . Detecting white matter injury in sickle cell disease using voxel-based morphometry . ANN NEUROL vol. 59 , ( 4 ) 662 - 672 .

Lusher J, Elander J, Bevan D, Fer PT, Burton B ( 2006 ) . Analgesic addiction and pseudoaddiction in painful chronic illness . CLIN J PAIN vol. 22 , ( 3 ) 316 - 324 .

WONKE B, HOFFBRAND AV, BOULOUX P, JENSEN C, TELFER P ( 1998 ) . New Approaches to the Management of Hepatitis and Endocrine Disorders in Cooley's Anemia . Annals of the New York Academy of Sciences . vol. 850 , 232 - 241 .

TELFER PT, Prengler M, Hogan A, Kirkham F, de Haan M, Vargha-Khadem F, Lane R ( 2006 ) . An exploratory study of physiological correlates of neurodevelopmental delay in infants with sickle cell anemia . British Journal of Haematology. vol. 132 , 99 - 107 .

Baldeweg T, Hogan AM, Saunders DE, Telfer P, Gadian DG, Vargha-Khadem F, Kirkham FJ ( 2006 ) . White matter injury in children with sickle cell disease detected using voxel-based morphometry . DEV MED CHILD NEUROL vol. 48 , 13 - 13 .

TELFER PT, Kirkham F, Hogan A, Saunders D, Baldeweg T, Vargha-Khadem F, Gadian D ( 2006 ) . White matter injury in children with sickle cell disease detected using voxel-based morphometry . Ann Neurol. vol. 59 , 662 - 672 .

Devereux H, Telfer P, Lee C, Dusheiko G ( 2005 ) . Hepatitis C genotypes in hemophilic patients treated with alpha‐interferon . Journal of Medical Virology vol. 45 , ( 3 ) 284 - 287 .

Kotecha K, Prengler M, Saunders DE, Hewes DKM, Kirkham FJ, Paul T ( 2005 ) . Change over Time of Transcranial Doppler Cerebral Blood Flow Velocity and the Relationship with Turbulence on Magnetic Resonance Angiography in Patients with Sickle Cell Anemia . Blood vol. 106 , ( 11 )

New HV, Cale CM, Tischkowitz M, Jones A, Telfer P, Veys P, D'Andrea A, Mathew CG et al. ( 2005 ) . Nijmegen breakage syndrome diagnosed as Fanconi anaemia . PEDIATR BLOOD CANCER vol. 44 , ( 5 ) 494 - 499 .

Lehal R, Davies C, Morrison I, Newell K, John Y, Mackay L, Challands J, Telfer P ( 2005 ) . Evaluation of intranasal diamorphine together with oral morphine for management of acute sickle pain in children . BRITISH JOURNAL OF HAEMATOLOGY . vol. 129 , 73 - 73 .

Telfer PT, Coen P, Chakravorty S, Wilkey O, Newell K, Evans J, Kirkham F ( 2005 ) . Survival and neurological complications in children with sickle cell disorders: data from an East London neonatal cohort . BRITISH JOURNAL OF HAEMATOLOGY . vol. 129 , 83 - 83 .

Telfer P, Constantinidou G, Andreou P, Christou S, Modell B, Angastiniotis M ( 2005 ) . Quality of life in thalassemia . COOLEY'S ANEMIA EIGHTH SYMPOSIUM . Editors: Vichinsky, EP , vol. 1054 , 273 - 282 .

Chakravorty S, Newell K, Ramchandani J, Qureshi K, Ibrahim R, Datta B, Telfer PT ( 2004 ) . Sickle cell disease pain in London and the Caribbean . Arch Dis Child vol. 89 , ( 3 ) 272 - 273 .

Elander J, Lusher J, Bevan D, Telfer P, Burton B ( 2004 ) . Understanding the causes of problematic pain management in sickle cell disease: Evidence that pseudoaddiction plays a more important role than genuine analgesic dependence . J PAIN SYMPTOM MANAG vol. 27 , ( 2 ) 156 - 169 .

Telfer PT, Garson JA, Whitby K, Grant PR, Yardumian A, Hoffbrand AV, Wonke B ( 2003 ) . Combination therapy with interferon alpha and ribavirin for chronic hepatitis C virus infection in thalassaemic patients . British Journal of Haematology vol. 98 , ( 4 ) 850 - 855 .

McDonald CP, Barbara JAJ, Hewitt PE, Hartley S, Telfer P, Gale R, James E, Prentice HG ( 2003 ) . Yersinia enterocolitica transmission from a red cell unit 34 days old . Transfusion Medicine vol. 6 , ( 1 ) 61 - 63 .

Davies JK, Telfer P, Cavenagh JD, Foot N, Neat M ( 2003 ) . Autoimmune cytopenias in the 22q11.2 deletion syndrome . Clin Lab Haematol vol. 25 , ( 3 ) 195 - 197 .

Rees DC, Olujohungbe AD, Parker NE, Stephens AD, Telfer P, Wright J ( 2003 ) . Guidelines for the management of the acute painful crisis in sickle cell disease . BRIT J HAEMATOL vol. 120 , ( 5 ) 744 - 752 .

TELFER PT, Bevan D, Lusher J, Elander J ( 2003 ) . Pain managaement and symptoms of substance dependence among patients with sickle cell disease . Social Sciences and Medicine vol. 57 , 1683 - 1696 .

Telfer P, De la Salle B, Ridler C ( 2001 ) . Antenatal testing for haemoglobinopathies . British Journal of Haematology vol. 110 , ( 4 ) 1003 - 1004 .

Telfer PT, Prestcott E, Holden S, Walker M, Hoffbrand AV, Wonke B ( 2001 ) . Hepatic iron concentration combined with long‐term monitoring of serum ferritin to predict complications of iron overload in thalassaemia major . British Journal of Haematology vol. 110 , ( 4 ) 971 - 977 .

Gupta V, Bremner FD, Telfer P ( 2001 ) . Bilateral retinal haemorrhages: an unusual presentation of pernicious anaemia . Br J Haematol vol. 112 , ( 4 )

TELFER PT, Pearson TC, Doughty H, Win N, Wild BJ ( 2001 ) . Hyperhemolytic transfusion reaction in sickle cell disease . Transfusion vol. 41 , 323 - 328 .

Kottaridis P, Peggs K, Lawrence A, Verfuerth S, Chatterjee R, Telfer P, Porter J, Mackinnon S et al. ( 2000 ) . One antigen mismatched related donor bone marrow transplant in a patient with acute lymphoblastic leukaemia and β-thalassaemia major: potential cure of both marrow disorders . Bone Marrow Transplantation vol. 25 , ( 6 ) 677 - 678 .

Tricta F, Spino M ( 1998 ) . Iron Chelation with Oral Deferiprone in Patients with Thalassemia . New England Journal of Medicine vol. 339 , ( 23 ) 1710 - 1714 .

Wonke B, Telfer P, Hoffbrand AV ( 1998 ) . Iron chelation with oral deferiprone in patients with thalassemia . New England Journal of Medicine vol. 339 , ( 23 )

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